Familial Adenomatous Polyposis Associated with Gastrointestinal Stromal Tumor: Report of a Case | oneFAPvoice

welcome to oneFAPvoice

- a positively charged Familial Adenomatous Polyposis community.
  • join today!
scientific articles

Familial Adenomatous Polyposis Associated with Gastrointestinal Stromal Tumor: Report of a Case

key information

source: The Turkish journal of gastroenterology

year: 2012

authors: Cumhur İbrahim Başsorgun, İrem Hicran Özbudak, Gülgün Erdoğan, Gülsüm Özlem Elpek, Tekinalp Gelen, Okan Erdoğan


Desmoid tumors are one of the most common extracolonic manifestations of the familial adenomatous polyposis. However, other soft tissue tumors are seen rarely in patients with familial adenomatous polyposis, including gastrointestinal stromal tumor. There is only one case reported in the literature. We describe a 29-year-old female who developed ileal malignant gastrointestinal stromal tumor 15 months after proctocolectomy for familial adenomatous polyposis, with a review of the literature focusing on sarcomas arising in this inherited disease. We suggest that the rare occurrence of gastrointestinal stromal tumor in familial adenomatous polyposis does not exclude their consideration in the differential diagnosis of extracolonic manifestations of the disease.

organization: Akdeniz University

read more full text source

To improve your experience on this site, we use cookies. This includes cookies essential for the basic functioning of our website, cookies for analytics purposes, and cookies enabling us to personalize site content. By clicking on 'Accept' or any content on this site, you agree that cookies can be placed. You may adjust your browser's cookie settings to suit your preferences.
More information

The cookie settings on this website are set to "allow cookies" to give you the best browsing experience possible. If you continue to use this website without changing your cookie settings or you click "Accept" below then you are consenting to this.